Spinal Epidural Venous Plexus Pathology in Hirayama Disease

Authors

Mathew B. Macey
Doreen T. Ho
Christopher M. Parres, Henry Ford HealthFollow
Juan E. Small

Recommended Citation

Macey MB, Ho DT, Parres CM, and Small JE. Spinal Epidural Venous Plexus Pathology in Hirayama Disease. J Clin Neuromuscul Dis 2019; 21(1):47-51.

Document Type

Article

Publication Date

9-1-2019

Publication Title

J Clin Neuromuscul Dis

Abstract

Hirayama disease is a rare juvenile amyotrophy that is often misdiagnosed as an unrelated, relentlessly progressive disease. We present the case of an 18-year-old man who presented with weakness and atrophy of the right forearm and hand. Dynamic cervical magnetic resonance imaging was used, revealing the classic findings of epidural venous plexus dilation and anterior displacement of the dural sac. In addition, dilation of the external vertebral venous plexus was visualized. We discuss the clinical utility of dynamic magnetic resonance imaging and the underlying pathophysiology of these findings in Hirayama disease.

PubMed ID

31453855

Volume

21

Issue

1

First Page

47

Last Page

51